000 03902nam a22003855i 4500
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003 MX-SnUAN
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007 cr nn 008mamaa
008 150903s2010 xxu| o |||| 0|eng d
020 _a9781603275248
_99781603275248
024 7 _a10.1007/9781603275248
_2doi
035 _avtls000343264
039 9 _a201509030845
_bVLOAD
_c201405050254
_dVLOAD
_y201402061151
_zstaff
040 _aMX-SnUAN
_bspa
_cMX-SnUAN
_erda
050 4 _aRC799-869
100 1 _aMurray, Karen F.
_eeditor.
_9319237
245 1 0 _aFibrocystic Diseases of the Liver /
_cedited by Karen F. Murray, Anne M. Larson.
264 1 _aTotowa, NJ :
_bHumana Press,
_c2010.
300 _axii, 640 páginas 161 ilustraciones, 70 ilustraciones en color.
_brecurso en línea.
336 _atexto
_btxt
_2rdacontent
337 _acomputadora
_bc
_2rdamedia
338 _arecurso en línea
_bcr
_2rdacarrier
347 _aarchivo de texto
_bPDF
_2rda
490 0 _aClinical Gastroenterology
500 _aSpringer eBooks
505 0 _aPathophysiology and Development -- Embryology and Development of the Ductal Plate -- Cholangiocyte Biology as Relevant to Cystic Liver Diseases -- Cholangiocyte Cilia and Basal Bodies -- Genetics of Fibrocystic Diseases of the Liver and Molecular Approaches to Therapy -- Diagnosis -- Radiologic Findings in the Fibrocystic Diseases -- Pathology of Fibrocystic Diseases of the Liver -- Disease States -- Alagille Syndrome and JAGGED1/NOTCH Sequence -- Biliary Atresia and the Ductal Plate -- Nephronophthisis and Renal–Hepatic–Pancreatic Dysplasia of Ivemark -- Meckel and Joubert Syndromes -- Bardet–Biedl and Jeune Syndromes -- Congenital Disorders of Glycosylation and Their Effects on the Liver -- Autosomal Recessive Polycystic Kidney Disease -- Caroli Disease, Caroli Syndrome, and Congenital Hepatic Fibrosis -- Simple Hepatic Cysts/Choledochal Cysts -- Autosomal Dominant Polycystic Liver Disease -- Echinococcal/Hydatid Cysts of the Liver -- Miscellaneous Cystic Lesions of the Liver -- Complications -- Vascular Complications of Fibrocystic Liver Disease -- Biliary Cystadenoma and Cystadenocarcinoma -- Cholangitis -- Surgical Management -- Surgical Management of Fibrocystic Liver Disease.
520 _aIn recent years there have been huge advances in the understanding of the genetic and molecular basis of the fibrocystic diseases. This volume provides a thorough review of fibrocyctic diseases that affect the liver. It contains in-depth discussions of the genetics, molecular biology, pathogenesis, histology, clinical presentations, complications of, treatment, and prognosis of the conditions affecting children and adults, and hence will be the gold-standard reference for these conditions. In addition, the histological features that distinguish these conditions from other potentially fibrosing hepatopathies are illustrated. Conditions with syndromic features involving the kidney or other organ systems are also reviewed. Thorough review of the clinical phenotypes, their presentations, treatment, potential complications of, and prognosis is discussed. Fibrocystic Diseases of the Liver will be an invaluable resource for hepatologists, gastroenterologists, nephrologists, and hepatic surgeons who care for children and adults with liver disease, as well as basic scientists in molecular genetics, hepatobiliary pathophysiology, hepatology and nephrology.
590 _aPara consulta fuera de la UANL se requiere clave de acceso remoto.
700 1 _aLarson, Anne M.
_eeditor.
_9319238
710 2 _aSpringerLink (Servicio en línea)
_9299170
776 0 8 _iEdición impresa:
_z9781603275231
856 4 0 _uhttp://remoto.dgb.uanl.mx/login?url=http://dx.doi.org/10.1007/978-1-60327-524-8
_zConectar a Springer E-Books (Para consulta externa se requiere previa autentificación en Biblioteca Digital UANL)
942 _c14
999 _c289161
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